MyoD-family inhibitor proteins act as auxiliary subunits of Piezo channels

Science. 2023 Aug 18;381(6659):799-804. doi: 10.1126/science.adh8190. Epub 2023 Aug 17.

Abstract

Piezo channels are critical cellular sensors of mechanical forces. Despite their large size, ubiquitous expression, and irreplaceable roles in an ever-growing list of physiological processes, few Piezo channel-binding proteins have emerged. In this work, we found that MyoD (myoblast determination)-family inhibitor proteins (MDFIC and MDFI) are PIEZO1/2 interacting partners. These transcriptional regulators bind to PIEZO1/2 channels, regulating channel inactivation. Using single-particle cryogenic electron microscopy, we mapped the interaction site in MDFIC to a lipidated, C-terminal helix that inserts laterally into the PIEZO1 pore module. These Piezo-interacting proteins fit all the criteria for auxiliary subunits, contribute to explaining the vastly different gating kinetics of endogenous Piezo channels observed in many cell types, and elucidate mechanisms potentially involved in human lymphatic vascular disease.

MeSH terms

  • Animals
  • Cryoelectron Microscopy
  • HEK293 Cells
  • Humans
  • Ion Channel Gating
  • Ion Channels* / chemistry
  • Ion Channels* / genetics
  • Ion Channels* / metabolism
  • Kinetics
  • Lymphatic Diseases / genetics
  • Mice
  • Mutation
  • Myoblasts / metabolism
  • Myogenic Regulatory Factors* / chemistry
  • Myogenic Regulatory Factors* / genetics
  • Myogenic Regulatory Factors* / metabolism
  • Protein Domains

Substances

  • Ion Channels
  • MDFIC protein, human
  • Myogenic Regulatory Factors
  • PIEZO1 protein, human