Severe Cytokine Release Syndrome and Immune Effector Cell-associated Neurotoxicity Syndrome in a Man Receiving Immune Checkpoint Inhibitors for Lung Cancer

Intern Med. 2024 May 1;63(9):1261-1267. doi: 10.2169/internalmedicine.2429-23. Epub 2023 Sep 15.

Abstract

A 55-year-old man with stage IV lung adenocarcinoma was treated with cisplatin, pemetrexed, nivolumab, and ipilimumab. Approximately 100 days after treatment initiation, he became disoriented and presented to the emergency department with a high fever. Blood tests revealed liver and kidney dysfunctions. Subsequently, the patient developed generalized convulsions that required intensive care. He was clinically diagnosed with cytokine release syndrome (CRS) and immune effector cell-associated neurotoxicity syndrome (ICANS). Organ damage was gradually controlled with immunosuppressive drugs, including steroids, and the patient was discharged. Successful treatment is rare in patients with CRS, including ICANS, during immune checkpoint inhibitor treatment for solid tumors.

Keywords: cytokine release syndrome; immune checkpoint inhibitor; immune effector cell-associated neurotoxicity syndrome; ipilimumab; nivolumab.

Publication types

  • Case Reports

MeSH terms

  • Adenocarcinoma of Lung / drug therapy
  • Cytokine Release Syndrome* / chemically induced
  • Cytokine Release Syndrome* / drug therapy
  • Cytokine Release Syndrome* / etiology
  • Humans
  • Immune Checkpoint Inhibitors* / adverse effects
  • Immunosuppressive Agents / adverse effects
  • Immunosuppressive Agents / therapeutic use
  • Lung Neoplasms* / drug therapy
  • Male
  • Middle Aged
  • Neurotoxicity Syndromes* / diagnosis
  • Neurotoxicity Syndromes* / etiology
  • Nivolumab / adverse effects

Substances

  • Immune Checkpoint Inhibitors
  • Immunosuppressive Agents
  • Nivolumab
  • cell-associated neurotoxicity