Adult presentation of unilateral pulmonary artery atresia in association with contralateral branch pulmonary stenosis is rare. We present the case of a quadragenarian, who manifested with right ventricular failure and hemoptysis. This report discusses the diagnostic workup and therapeutic options along with a brief overview of the concerned literature.
Keywords: Adult-onset congenital heart disease; multimodality imaging; peripheral pulmonary stenosis; pulmonary angioplasty; unilateral pulmonary artery atresia.
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