Transcatheter Closure of Superior Sinus Venosus Defects

JACC Cardiovasc Interv. 2023 Nov 13;16(21):2587-2599. doi: 10.1016/j.jcin.2023.07.024. Epub 2023 Oct 18.

Abstract

Superior sinus venosus defect is a communication between the right and left atrium located above the upper margin of the oval fossa, immediately inferior to the junction of the superior vena cava and the right atrium. It is systematically associated with partial anomalous pulmonary venous drainage, especially of the right upper pulmonary vein. Surgical repair has been the gold standard approach to close that defect. Introduced in 2014, percutaneous closure has gradually become a safe and effective alternative to surgery in carefully selected patients, although worldwide experience remains limited. This article provides an appraisal of the patients' selection process and a step-by-step description of the procedure as well as a comprehensive review of its outcomes.

Keywords: 3-dimensional technology; congenital heart disease; multimodal fusion imaging; sinus venosus defect; transcatheter closure.

Publication types

  • Review
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Heart Septal Defects, Atrial* / surgery
  • Heart Septal Defects, Atrial* / therapy
  • Humans
  • Pulmonary Veins* / abnormalities
  • Pulmonary Veins* / diagnostic imaging
  • Pulmonary Veins* / surgery
  • Treatment Outcome
  • Vena Cava, Superior / diagnostic imaging

Supplementary concepts

  • Atrial Septal Defect Sinus Venosus