Case Report: Infant-onset Degos disease with nervous system involvement and a literature review

Xin-Wei Shi; Jiang-Hong Deng; Cai-Feng Li

doi:10.3389/fped.2024.1374150

Case Report: Infant-onset Degos disease with nervous system involvement and a literature review

Front Pediatr. 2024 Jul 5:12:1374150. doi: 10.3389/fped.2024.1374150. eCollection 2024.

Authors

Xin-Wei Shi¹, Jiang-Hong Deng¹, Cai-Feng Li¹

Affiliation

¹ Department of Rheumatology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Abstract

Degos disease also known as malignant atrophic papulosis (MAP), is an autoinflammatory disease that mainly affects small- to medium-sized arteries. Gastrointestinal and nervous system are most commonly affected systems. Herein, we reported a case of Degos disease with disease onset during infantile and had severe neurological involvement.

Keywords: Degos disease; infantile onset; malignant atrophic papulosis; neurological involvement; prognosis.

Publication types

Case Reports

Grants and funding

The author(s) declare that no financial support was received for the research, authorship, and/or publication of this article.