Complex Congenital Anomalies: A Case Report of Left Pulmonary Hypoplasia, Absent Left Pulmonary Artery, and Congenital Heart Disease in an 11-Month-Old Male Child

Cureus. 2024 Jun 28;16(6):e63430. doi: 10.7759/cureus.63430. eCollection 2024 Jun.

Abstract

A rare disorder called pulmonary hypoplasia is characterized by inadequate lung development, which frequently results in respiratory dysfunction and other related abnormalities. We present a case of an 11-month-old male child with left lung hypoplasia, absent left pulmonary artery, and ventricular septal defect (VSD). The child exhibited symptoms of cough and cold, with a history of recurrent respiratory tract infections since birth. Cardiovascular examination revealed a pan systolic murmur consistent with VSD, while respiratory examination indicated decreased air entry on the left side. Imaging studies confirmed the absence of the left pulmonary artery and left lung hypoplasia. Despite recommendations for VSD surgery, the child's parents declined surgical intervention, leading to discharge against medical advice. This case highlights the challenges in managing pulmonary hypoplasia, especially when accompanied by complex congenital heart defects, and underscores the importance of multidisciplinary care and parental involvement in decision-making.

Keywords: clinical cardiology; congenital cardiac anomalies; pulmonary artery; pulmonary hypoplasia; ventricular septal defect (vsd).

Publication types

  • Case Reports