Airway-derived emphysema-specific alveolar type II cells exhibit impaired regenerative potential in COPD

Eur Respir J. 2024 Dec 5;64(6):2302071. doi: 10.1183/13993003.02071-2023. Print 2024 Dec.

Abstract

Emphysema, the progressive destruction of gas exchange surfaces in the lungs, is a hallmark of COPD that is presently incurable. This therapeutic gap is largely due to a poor understanding of potential drivers of impaired tissue regeneration, such as abnormal lung epithelial progenitor cells, including alveolar type II (ATII) and airway club cells. We discovered an emphysema-specific subpopulation of ATII cells located in enlarged distal alveolar sacs, termed asATII cells. Single-cell RNA sequencing and in situ localisation revealed that asATII cells co-express the alveolar marker surfactant protein C and the club cell marker secretaglobin-3A2 (SCGB3A2). A similar ATII subpopulation derived from club cells was also identified in mouse COPD models using lineage labelling. Human and mouse ATII subpopulations formed 80-90% fewer alveolar organoids than healthy controls, indicating reduced progenitor function. Targeting asATII cells or their progenitor club cells could reveal novel COPD treatment strategies.

MeSH terms

  • Alveolar Epithelial Cells* / metabolism
  • Animals
  • Disease Models, Animal
  • Female
  • Humans
  • Male
  • Mice
  • Middle Aged
  • Organoids
  • Pulmonary Alveoli / cytology
  • Pulmonary Alveoli / pathology
  • Pulmonary Disease, Chronic Obstructive* / metabolism
  • Pulmonary Disease, Chronic Obstructive* / physiopathology
  • Pulmonary Emphysema* / metabolism
  • Pulmonary Emphysema* / physiopathology
  • Pulmonary Surfactant-Associated Protein C / metabolism
  • Regeneration*
  • Stem Cells / cytology
  • Stem Cells / metabolism
  • Uteroglobin / genetics
  • Uteroglobin / metabolism

Substances

  • Pulmonary Surfactant-Associated Protein C
  • Uteroglobin