The Modified S-GRAS Scoring System for Prognosis in Korean with Adrenocortical Carcinoma

Endocrinol Metab (Seoul). 2024 Oct;39(5):803-812. doi: 10.3803/EnM.2024.2086. Epub 2024 Sep 25.

Abstract

Backgruound: Adrenocortical carcinomas (ACCs) are rare tumors with aggressive but varied prognosis. Stage, Grade, Resection status, Age, Symptoms (S-GRAS) score, based on clinical and pathological factors, was found to best stratify the prognosis of European ACC patients. This study assessed the prognostic performance of modified S-GRAS (mS-GRAS) scores including modified grade (mG) by integrating mitotic counts into the Ki67 index (original grade), in Korean ACC patients.

Methods: Patients who underwent surgery for ACC between January 1996 and December 2022 at three medical centers in Korea were retrospectively analyzed. mS-GRAS scores were calculated based on tumor stage, mG (Ki67 index or mitotic counts), resection status, age, and symptoms. Patients were divided into four groups (0-1, 2-3, 4-5, and 6-9 points) based on total mS-GRAS score. The associations of each variable and mS-GRAS score with recurrence and survival were evaluated using Cox regression analysis, Harrell's concordance index (C-index), and the Kaplan-Meier method.

Results: Data on mS-GRAS components were available for 114 of the 153 patients who underwent surgery for ACC. These 114 patients had recurrence and death rates of 61.4% and 48.2%, respectively. mS-GRAS score was a significantly better predictor of recurrence (C-index=0.829) and death (C-index=0.747) than each component (P<0.05), except for resection status. mS-GRAS scores correlated with shorter progression-free survival (P=8.34E-24) and overall survival (P=2.72E-13).

Conclusion: mS-GRAS scores showed better prognostic performance than tumor stage and grade in Asian patients who underwent surgery for ACC.

Keywords: Adrenocortical carcinoma; Prognosis; Recurrence; Survival analysis.

MeSH terms

  • Adrenal Cortex Neoplasms* / mortality
  • Adrenal Cortex Neoplasms* / pathology
  • Adrenal Cortex Neoplasms* / surgery
  • Adrenocortical Carcinoma* / mortality
  • Adrenocortical Carcinoma* / pathology
  • Adrenocortical Carcinoma* / surgery
  • Adult
  • Aged
  • Female
  • Humans
  • Male
  • Middle Aged
  • Neoplasm Grading
  • Neoplasm Recurrence, Local / pathology
  • Neoplasm Staging
  • Prognosis
  • Republic of Korea / epidemiology
  • Retrospective Studies
  • Survival Rate
  • Young Adult