A neuro-lymphatic communication guides lymphatic development by CXCL12 and CXCR4 signaling

Development. 2024 Nov 15;151(22):dev202901. doi: 10.1242/dev.202901. Epub 2024 Nov 26.

Abstract

Lymphatic vessels grow through active sprouting and mature into a vascular complex that includes lymphatic capillaries and collecting vessels that ensure fluid transport. However, the signaling cues that direct lymphatic sprouting and patterning remain unclear. In this study, we demonstrate that chemokine signaling, specifically through CXCL12 and CXCR4, plays crucial roles in regulating lymphatic development. We show that LEC-specific Cxcr4-deficient mouse embryos and CXCL12 mutant embryos exhibit severe defects in lymphatic sprouting, migration and lymphatic valve formation. We also discovered that CXCL12, originating from peripheral nerves, directs the migration of dermal lymphatic vessels to align with nerves in developing skin. Deletion of Cxcr4 or blockage of CXCL12 and CXCR4 activity results in reduced VEGFR3 levels on the LEC surface. This, in turn, impairs VEGFC-mediated VEGFR3 signaling and downstream PI3K and AKT activities. Taken together, these data identify previously unknown chemokine signaling originating from peripheral nerves that guides dermal lymphatic sprouting and patterning. Our work identifies for the first time a neuro-lymphatics communication during mouse development and reveals a previously unreported mechanism by which CXCR4 modulates VEGFC, VEGFR3 and AKT signaling.

Keywords: CXCL12/CXCR4; Chemokine signaling; Lymphangiogenesis; Lymphatic development; Peripheral nerves; VEGFC/VEGFR3.

MeSH terms

  • Animals
  • Cell Movement
  • Chemokine CXCL12* / genetics
  • Chemokine CXCL12* / metabolism
  • Endothelial Cells / metabolism
  • Lymphangiogenesis / genetics
  • Lymphatic Vessels* / embryology
  • Lymphatic Vessels* / metabolism
  • Mice
  • Mice, Knockout
  • Phosphatidylinositol 3-Kinases / metabolism
  • Proto-Oncogene Proteins c-akt / metabolism
  • Receptors, CXCR4* / genetics
  • Receptors, CXCR4* / metabolism
  • Signal Transduction*
  • Vascular Endothelial Growth Factor C / genetics
  • Vascular Endothelial Growth Factor C / metabolism
  • Vascular Endothelial Growth Factor Receptor-3* / genetics
  • Vascular Endothelial Growth Factor Receptor-3* / metabolism

Substances

  • Receptors, CXCR4
  • Chemokine CXCL12
  • Vascular Endothelial Growth Factor Receptor-3
  • CXCR4 protein, mouse
  • Cxcl12 protein, mouse
  • Vascular Endothelial Growth Factor C
  • Proto-Oncogene Proteins c-akt
  • Phosphatidylinositol 3-Kinases