Chronic Thromboembolic Pulmonary Artery Hypertension or Fibrosing Mediastinitis?

Lamk Kadiyani; Umadevi Karuru; Shyam Sunder Kothari; Sivasubramanian Ramakrishnan; Saurabh Kumar Gupta; Velayudham Devagouru; Chetan D Patel

doi:10.1016/j.jaccas.2024.102569

Chronic Thromboembolic Pulmonary Artery Hypertension or Fibrosing Mediastinitis?

JACC Case Rep. 2024 Oct 2;29(19):102569. doi: 10.1016/j.jaccas.2024.102569.

Authors

Lamk Kadiyani¹, Umadevi Karuru¹, Shyam Sunder Kothari¹, Sivasubramanian Ramakrishnan¹, Saurabh Kumar Gupta¹, Velayudham Devagouru², Chetan D Patel³

Affiliations

¹ Department of Cardiology, All India Institute of Medical Sciences, Delhi, India.
² Department of Cardiac, Thoracic and Vascular Surgery, All India Institute of Medical Sciences, Delhi, India.
³ Department of Nuclear Medicine, All India Institute of Medical Sciences, Delhi, India.

Abstract

We report a case of pulmonary hypertension in association with right heart thrombus and mediastinal lymphadenopathy leading to the diagnostic dilemma of chronic thromboembolic pulmonary hypertension vs fibrosing mediastinitis despite of extensive noninvasive workup, considering different treatment strategies and therapeutic implications. Surgical findings provided a conclusive diagnosis and excellent prognosis.

Keywords: chronic thromboembolic pulmonary hypertension; fibrosing mediastinitis; pulmonary embolism; pulmonary hypertension; tuberculosis.

Publication types

Case Reports