Infratentorial superficial siderosis

Ugeskr Laeger. 2024 Oct 21;186(43):V03240230. doi: 10.61409/V03240230.
[Article in Danish]

Abstract

Infratentorial superficial siderosis is a neurological condition that results from hemosiderin deposition on the surface of the brain and spinal cord. This article considers iSS, a potentially disabling disorder usually associated with prolonged persistent, or intermittent subarachnoid bleeding from a dural defect, and characterised by progressive hearing loss and vestibular impairment, ataxia, and myelopathy. There are numerous diagnostic challenges and complex neurological impairments in iSS, but we have, in this case report, tried to present the importance of a multidisciplinary approach involving key teams.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Female
  • Hemosiderin / analysis
  • Hemosiderin / metabolism
  • Hemosiderosis* / diagnosis
  • Hemosiderosis* / pathology
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Siderosis / diagnosis
  • Subarachnoid Hemorrhage* / diagnosis
  • Subarachnoid Hemorrhage* / diagnostic imaging

Substances

  • Hemosiderin