Kommerell's diverticulum with an aberrant subclavian artery is a rare congenital aortic arch anomaly. Therefore surgical indication and strategy are not well established. A 43-year-old man was referred to our hospital with a chief complaint of chest and back pain. Contrast-enhanced computed tomography (CT) scan revealed Kommerell's diverticulum and aberrant right subclavian artery( ARSA) with Stanford type B acute aortic dissection. Aortic dissection involved Kommerell's diverticulum and ARSA. We performed total arch replacement with frozen elephant trunk technique and ARSA embolization. The postoperative course was uneventful. Contrast-enhanced CT scan revealed thrombosed Kommerell's diverticulum and closure of the primary tear. This surgical approach would be an effective treatment option for Kommerell's diverticulum with an aberrant subclavian artery.