Seckel's syndrome, also known as bird-headed dwarf of Seckel or nanocephalic dwarf, occurs very rarely within the field of orthopaedic diseases. 20 cases only have been described in literature so far. The article gives a detailed explanation of the syndrome. In the two patients discussed here, the specifically orthopaedic aspect follows from an accompanying coxa vara infantum with shearing of the epiphysis of the femoral head. The article describes the pre-operative and post-operative clinical and roentgenological findings.