Serum immunoglobulins and lymphocyte subpopulations derangement in Turner's syndrome

J Immunogenet. 1981 Oct;8(5):337-44. doi: 10.1111/j.1744-313x.1981.tb00938.x.

Abstract

Abnormalities of the proportions of peripheral blood lymphocyte subpopulations and of immunoglobulin serum levels were found in twenty patients affected by Turner's syndrome. A slight but significantly decreased percentage of circulating T and B cells, and increased percentage of null cells and a decreased in vitro responsiveness of lymphocytes to phytohaemagglutinin, concanavalin A and pokeweed mitogen were found in Turner's syndrome patients. IgG serum level was found significantly decreased in comparison with age-matched fifty-seven normal males and fifty-seven normal females and IgM serum level was intermediate between female and male values; Turner's syndrome patients with monosomy had an IgM serum concentration very close to male values. The derangement of T and B lymphocyte subpopulations, probably related to the aneuploidy, does not seem to be a severe one but it could account for the immunoglobulin abnormalities and for the association of Turner's syndrome with immunological disorders such as autoimmune diseases. The role of X chromosome on IgM serum level is discussed.

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Female
  • Humans
  • Immunoglobulin A / analysis
  • Immunoglobulin G / analysis
  • Immunoglobulin M / analysis
  • Immunoglobulins / analysis*
  • Lectins / pharmacology
  • Leukocyte Count
  • Lymphocyte Activation
  • Lymphocytes* / immunology
  • Turner Syndrome / blood*
  • Turner Syndrome / immunology

Substances

  • Immunoglobulin A
  • Immunoglobulin G
  • Immunoglobulin M
  • Immunoglobulins
  • Lectins