Crkl is complexed with tyrosine-phosphorylated Cbl in Ph-positive leukemia

J Biol Chem. 1995 Sep 15;270(37):21468-71. doi: 10.1074/jbc.270.37.21468.

Abstract

The deregulated tyrosine kinase activity of the Bcr/Abl protein has been causally linked to the development of Philadelphia (Ph) chromosome-positive leukemia in mice and man. Abnormally tyrosine-phosphorylated substrates of the Bcr/Abl kinase in Ph-positive cells are likely to contribute to leukemogenesis by interfering with normal signal transduction pathways. We have previously shown that the adaptor molecule Crkl is a major in vivo substrate for the Bcr/Abl tyrosine kinase, and it is thought to connect Bcr/Abl with downstream effectors. In the current study, a tyrosine-phosphorylated protein with a molecular mass of approximately 120 kDa was identified which binds only to the Crkl Src homology 2 (SH2) domain in cells, including Ph-positive patient material, containing an active Bcr/Abl protein. We demonstrate here that this protein is Cbl, originally discovered as an oncogene which induces B-cell and myeloid leukemias in mice. The Crkl SH2 domain binds specifically to Cbl. The Src homology 3 (SH3) domains of Crkl do not bind to Cbl, but do bind Bcr/Abl. These findings suggest the existence of a trimolecular complex involving Bcr/Abl, Crkl, and Cbl and are consistent with a model in which Crkl mediates the oncogenic signal of Bcr/Abl to Cbl.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adaptor Proteins, Signal Transducing*
  • Animals
  • Binding Sites
  • Cell Line
  • Electrophoresis, Polyacrylamide Gel
  • Fusion Proteins, bcr-abl / metabolism
  • Glutathione Transferase / metabolism
  • Humans
  • Leukemia, Erythroblastic, Acute
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / blood
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / metabolism*
  • Mice
  • Molecular Weight
  • Nuclear Proteins / isolation & purification
  • Nuclear Proteins / metabolism*
  • Oncogene Protein v-cbl
  • Phosphorylation
  • Phosphotyrosine
  • Recombinant Fusion Proteins / metabolism
  • Retroviridae Proteins, Oncogenic / isolation & purification
  • Retroviridae Proteins, Oncogenic / metabolism*
  • Tumor Cells, Cultured
  • Tyrosine / analogs & derivatives
  • Tyrosine / analysis

Substances

  • Adaptor Proteins, Signal Transducing
  • CRKL protein
  • Nuclear Proteins
  • Oncogene Protein v-cbl
  • Recombinant Fusion Proteins
  • Retroviridae Proteins, Oncogenic
  • Phosphotyrosine
  • Tyrosine
  • Glutathione Transferase
  • Fusion Proteins, bcr-abl