Supravalvular aortic stenosis may be associated with arterial lesions. This condition is rare and its natural history is not well known. The authors report the case of a child operated in 1981 for supravalvular aortic stenosis and stenoses of the supraaortic vessels. The operation consisted of enlarging the ascending aorta with a patch and resection-reimplantation of both carotids without interposition of prosthetic material. Twelve years later, the haemodynamic result was the same as that of the postoperative control. This case tends to prove the low evolutive potential of this condition and the long term benefits of this surgical technique.