Activation of Ca-permeable cation channels by myocarditis-associated antibody in guinea pig ventricular myocytes

J Clin Invest. 1993 Mar;91(3):1231-4. doi: 10.1172/JCI116285.

Abstract

The pathogenesis of myocarditis and dilated cardiomyopathy is though to involve autoimmunological processes and myocardial calcium overload. Serum containing antiheart antibodies associated with a murine model of myocarditis increased [Ca2+]i in guinea pig ventricular myocytes only in the presence of extracellular Ca2+. The antiheart antibody-positive serum activated Ca(2+)-permeable cation channels that were insensitive to dihydropyridines and membrane stretch. The permeability sequence was Ba2+ > Ca2+ > Na+ approximately K+, and the single-channel conductance to Ba2+ was 12 pS. The channel was activated by extracellular application of the serum during on-cell recording, which suggests that a soluble intracellular messenger may be involved. The antibody-positive serum did not alter voltage-gated Ca2+ currents. We propose that excess Ca entry in myocarditis and dilated cardiomyopathy results from activation of a Ca(2+)-permeable cationic channel by the autoantibodies.

MeSH terms

  • Animals
  • Antibodies / blood
  • Antibodies / isolation & purification
  • Antibodies / pharmacology*
  • Barium / metabolism
  • Calcium / metabolism*
  • Cations
  • Fura-2
  • Guinea Pigs
  • Heart Ventricles
  • Ion Channels / physiology*
  • Male
  • Membrane Potentials
  • Mice
  • Mice, Inbred BALB C
  • Myocarditis / blood
  • Myocarditis / immunology*
  • Myocardium / immunology*
  • Myocardium / metabolism

Substances

  • Antibodies
  • Cations
  • Ion Channels
  • Barium
  • Calcium
  • Fura-2