Interaction of chromosome-6-encoded dystrophin related protein with the extracellular matrix

J Cell Sci. 1995 Jan:108 ( Pt 1):173-85. doi: 10.1242/jcs.108.1.173.

Abstract

Dystrophin-related protein/utrophin is a large, cytoskeletal protein that shares significant sequence similarity with dystrophin. Dystrophin-related protein is known to be enriched where cell-extracellular matrix contacts are well defined; however, the mechanism of dystrophin-related protein enrichment and its functional role(s) at these sites are yet to be defined. Here, we demonstrate that dystrophin-related protein is concentrated in patches of astrocyte membrane in apposition with the extracellular matrix and that the distribution of dystrophin-related protein is temporally modulated by the extracellular matrix constituent laminin. Furthermore, we demonstrate the existence of a specific biochemical association between dystrophin-related protein and laminin in astrocytes. In these astrocytes, the depletion of dystrophin-related protein by the use of antisense dystrophin-related protein oligonucleotides causes marked reduction in the formation of functional substratum-membrane attachments. Taken together, these data suggest that dystrophin-related protein may function in the generation and maintenance of regional substratum-associated membrane specializations, such as those found at the blood-brain barrier.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Astrocytes / metabolism*
  • Astrocytes / ultrastructure
  • Base Sequence
  • Brain / cytology
  • Brain / metabolism*
  • Cells, Cultured
  • Chromosome Mapping*
  • Cytoskeletal Proteins / analysis
  • Cytoskeletal Proteins / biosynthesis*
  • Cytoskeletal Proteins / genetics
  • Extracellular Matrix / metabolism*
  • Gene Expression*
  • Laminin / analysis
  • Laminin / metabolism
  • Membrane Proteins*
  • Mice
  • Mice, Inbred C57BL
  • Mice, Inbred mdx
  • Molecular Sequence Data
  • Oligonucleotides, Antisense / pharmacology
  • Rats
  • Rats, Sprague-Dawley
  • Utrophin

Substances

  • Cytoskeletal Proteins
  • Laminin
  • Membrane Proteins
  • Oligonucleotides, Antisense
  • Utrn protein, mouse
  • Utrophin