Is neuro-ectodermal differentiation of Ewing's sarcoma of bone associated with an unfavourable prognosis?

Eur J Cancer. 1995;31A(3):307-14. doi: 10.1016/0959-8049(94)00417-4.

Abstract

Among Ewing's sarcoma (ES) of bone and related entities are tumours with neuro-ectodermal features that could represent a biologically distinct type. In order to assess the prognostic significance of the various forms of ES, a retrospective joint study involving three cancer centres in Europe and the U.S.A. was initiated. The material from 315 primary ES was reviewed by a panel of five pathologists and classified as typical ES (220 cases), atypical ES (48 cases) or ES with neuro-ectodermal features (47 cases). Prognostic factor analysis on treatment failure-free survival was performed using the Cox model. It included histopathological classification, initial patient characteristics, clinical presentation and treatment type. After multivariate analysis, in addition to treatment type (P < 0.001), metastases (P = 0.003) and proximal tumour location (P = 0.006), two histopathological parameters correlated with poor treatment failure-free survival, the presence of filigree pattern (P = 0.044) and dark cells (P = 0.043). We conclude that ES with neuro-ectodermal features does not appear to have a different outcome to the other subtypes.

Publication types

  • Multicenter Study

MeSH terms

  • Adolescent
  • Adult
  • Analysis of Variance
  • Bone Neoplasms / pathology*
  • Bone Neoplasms / therapy
  • Cell Differentiation
  • Child
  • Child, Preschool
  • Disease-Free Survival
  • Female
  • Humans
  • Infant
  • Male
  • Middle Aged
  • Multivariate Analysis
  • Neuroectodermal Tumors, Primitive, Peripheral / pathology*
  • Neuroectodermal Tumors, Primitive, Peripheral / therapy
  • Prognosis
  • Retrospective Studies
  • Risk Factors
  • Sarcoma, Ewing / pathology*
  • Sarcoma, Ewing / therapy
  • Single-Blind Method