A biclonal large granular lymphocyte (LGL)/NK-associated (NKa) disorder of CD4+ and CD8+ lymphocyte subpopulations characterized by the simultaneous presence of distinct TCR rearrangements

Br J Haematol. 1994 Nov;88(3):629-32. doi: 10.1111/j.1365-2141.1994.tb05087.x.

Abstract

This communication reports a patient with concomitant expansions of CD4+ and CD8+ large granular lymphocytes. Immunological analyses revealed that the abnormally increased CD4+ LGL fraction was phenotypically similar to other reported persistent CD4+ LGL expansions, whereas the phenotypic profile for the CD8+ LGL component was unusual. Of particular note was the finding that both the CD4+ and CD8+ LGL fractions showed high membrane CD45RO isoform expression, thus suggesting their 'primed' status. Molecular biology studies of immunomagnetically fractionated cells using a T gamma 9 TCR gamma gene primer further revealed that the CD4+ and CD8+ components were both clonal but showed different patterns of rearrangement. It is suggested that the simultaneous presence of CD4+ and CD8+ clonal populations are unlikely to have been derived from a common progenitor and that they reflect expansions of functionally restricted subpopulations.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Base Sequence
  • CD4-Positive T-Lymphocytes / pathology*
  • Clone Cells
  • Female
  • Gene Rearrangement, T-Lymphocyte*
  • Granulocytes / pathology*
  • Humans
  • Killer Cells, Natural / pathology
  • Leukocyte Common Antigens
  • Lymphoproliferative Disorders / genetics
  • Lymphoproliferative Disorders / pathology*
  • Molecular Sequence Data
  • T-Lymphocyte Subsets / pathology*

Substances

  • Leukocyte Common Antigens