Successful repair of the right atrial isomerism, double outlet right ventricle, common atrioventricular canal, pulmonary stenosis, and total anomalous pulmonary venous connection

J Card Surg. 1994 Jul;9(4):433-9. doi: 10.1111/j.1540-8191.1994.tb00873.x.

Abstract

A 6-year-old boy was successfully operated on for double outlet ventricle, common atrioventricular canal with severe valvular regurgitation, right atrial isomerism, L-loop ventricles, total anomalous pulmonary venous connection, and pulmonary stenosis with hypoplastic left pulmonary artery. The interventricular rerouting from the left ventricle to the ascending aorta was performed with a spiral patch, the interatrial switching was performed by a Mustard patch, the common atrioventricular orifice was partitioned and valve repair was performed, and an 18-mm valved conduit was inserted between the right ventricle and the pulmonary artery. Although the patient had a small residual ventricular septal defect and pulmonary stenosis, the patient is alive and well.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / surgery*
  • Cardiac Surgical Procedures / methods
  • Child
  • Double Outlet Right Ventricle / surgery
  • Heart Atria / abnormalities
  • Heart Defects, Congenital / surgery*
  • Heart Ventricles / abnormalities
  • Humans
  • Male
  • Pulmonary Valve Stenosis / surgery
  • Pulmonary Veins / abnormalities