Definitive cure of hyperammonemia by liver transplantation in urea cycle defects: report of three cases

Transplant Proc. 1994 Feb;26(1):188.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Amino Acid Metabolism, Inborn Errors / metabolism
  • Amino Acid Metabolism, Inborn Errors / surgery*
  • Ammonia / blood*
  • Argininosuccinate Synthase / deficiency
  • Child
  • Citrulline / blood
  • Humans
  • Liver Transplantation*
  • Ornithine Carbamoyltransferase Deficiency Disease
  • Urea / metabolism*

Substances

  • Citrulline
  • Ammonia
  • Urea
  • Argininosuccinate Synthase