A novel gene, AF-1p, fused to HRX in t(1;11)(p32;q23), is not related to AF-4, AF-9 nor ENL

Oncogene. 1994 Apr;9(4):1039-45.

Abstract

Most of the translocations affecting the chromosome band 11q23, frequently seen in human acute leukemias, involve a restricted area of the HRX gene. We have characterized two t(1;11)(p32;q11) translocations which fuse the HRX gene to a novel gene, AF-1p on chromosome 1p32, in two myeloid leukemias. The der (11) chromosome expresses the 1368 N-terminal amino acids of HRX, including the AT-hook, snRNP and methyltransferase similarities, fused to almost all the AF-1p product. The predicted wild type AF-1p product is a 98 kDa acidic protein which does not exhibit similarity to the AF-4, AF-9 and ENL gene products. It is highly similar to the murine eps 15 gene product, which encodes a cytoplasmic phosphoprotein. Our data indicate that AF-1p defines another class of genes fused to HRX in 11q23 abnormalities.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing
  • Adult
  • Amino Acid Sequence
  • Base Sequence
  • Blotting, Northern
  • Calcium-Binding Proteins*
  • Child, Preschool
  • Chromosomes, Human, Pair 1*
  • Chromosomes, Human, Pair 11*
  • Cloning, Molecular
  • Consensus Sequence
  • DNA-Binding Proteins / genetics*
  • Female
  • Histone-Lysine N-Methyltransferase
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Leukemia, Monocytic, Acute / genetics*
  • Leukemia, Myeloid / genetics*
  • Male
  • Molecular Sequence Data
  • Myeloid-Lymphoid Leukemia Protein
  • Phosphoproteins*
  • Polymerase Chain Reaction
  • Proto-Oncogenes*
  • Restriction Mapping
  • Transcription Factors*
  • Translocation, Genetic*
  • Zinc Fingers

Substances

  • Adaptor Proteins, Signal Transducing
  • Calcium-Binding Proteins
  • DNA-Binding Proteins
  • EPS15 protein, human
  • Intracellular Signaling Peptides and Proteins
  • KMT2A protein, human
  • Phosphoproteins
  • Transcription Factors
  • Myeloid-Lymphoid Leukemia Protein
  • Histone-Lysine N-Methyltransferase

Associated data

  • GENBANK/Z29064
  • GENBANK/Z29070