Further impairment of muscle phosphate kinetics by lengthening exercise in DMD/BMD carriers. An in vivo 31P-NMR spectroscopy study

J Neurol Sci. 1993 Oct;119(1):65-73. doi: 10.1016/0022-510x(93)90192-2.

Abstract

We used phosphorus magnetic resonance spectroscopy (31P-MRS) to study the effect of exercise-induced muscle injury in the calf muscle of 7 DMD/BMD carriers and 6 non-carrier females. All subjects performed 50-80 lengthening contractions with the right calf muscles. 48 h after lengthening exercise non-carriers showed increased sensitivity to pressure in their gastrocnemius accompanied by increased T2 relaxation times and by elevated Pi/PCr ratios at rest. DMD/BMD carriers did not show any effect of lengthening exercise on these measurements. In-magnet exercise revealed in all carriers a reduced initial rate of Pi recovery and an increased time to fully recovery the resting value of intracellular pH. Lengthening exercise further decreased the initial rate of Pi recovery. Non-carriers did not show any variation attributable to lengthening exercise either during in-magnet work or during recovery from exercise. We found that lengthening exercise contractions causes: (1) less muscle injury in carriers compared to non-carriers, (2) even slower rate of Pi recovery, but (3) no effect on Pi recovery in non-carriers. The use of lengthening exercise and measurements of Pi recovery may be a useful method to evaluate the disease process in DMD/BMD.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Exercise / physiology*
  • Female
  • Heterozygote
  • Humans
  • Hydrogen-Ion Concentration
  • Magnetic Resonance Imaging
  • Magnetic Resonance Spectroscopy
  • Male
  • Muscles / chemistry
  • Muscles / metabolism*
  • Muscles / pathology
  • Muscular Dystrophies / metabolism*
  • Muscular Dystrophies / pathology
  • Phosphates / metabolism*
  • Phosphocreatine / metabolism
  • Phosphorus Isotopes

Substances

  • Phosphates
  • Phosphorus Isotopes
  • Phosphocreatine