Lambda light chain deposition disease presenting as an amyloid-like arthropathy

J Rheumatol. 1993 May;20(5):880-4.

Abstract

We describe a case of lambda light chain deposition disease (LCDD) which presented with symmetric, seronegative, nonerosive arthritis associated with skin nodules and widespread, progressive soft tissue induration. Multiple biopsies disclosed Congo red nonbirefringent deposits which stained strongly with lambda light chain antiserum, allowing distinction from amyloid arthropathy. This is the first report of musculoskeletal involvement in LCDD.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Amyloidosis / diagnosis*
  • Diagnosis, Differential
  • Humans
  • Immunoglobulin Light Chains / metabolism*
  • Immunoglobulin lambda-Chains / metabolism*
  • Joint Diseases / diagnosis*
  • Male
  • Muscles / pathology
  • Paraproteinemias / diagnosis*
  • Paraproteinemias / pathology

Substances

  • Immunoglobulin Light Chains
  • Immunoglobulin lambda-Chains