Non-responsiveness of serum gonadotropins and testosterone to pulsatile GnRH in hemochromatosis suggesting a pituitary defect

Acta Endocrinol (Copenh). 1993 Apr;128(4):351-4. doi: 10.1530/acta.0.1280351.

Abstract

We investigated the potential pituitary origin of gonadal insufficiency in hemochromatosis. Gonadotropin secretion was studied in seven patients with hemochromatosis and hypogonadism, before and after chronic pulsatile GnRH therapy. Pulsatile LH secretion was studied before (sampling every 10 min for 6 h) and after 15-30 days of chronic pulsatile GnRH therapy (10-12 micrograms per pulse). Prior to GnRH therapy, all the patients had low serum testosterone, FSH and LH levels. LH secretion was non-pulsatile in four patients, while a single pulse was detected in the remaining three. Chronic pulsatile GnRH administration did not increase serum testosterone levels; similarly, serum LH levels remained low: neither pulse frequency nor pulse amplitude was modified. We conclude that hypogonadism in hemochromatosis is due to pituitary lesions.

MeSH terms

  • Adolescent
  • Adult
  • Follicle Stimulating Hormone / blood
  • Gonadotropin-Releasing Hormone / administration & dosage
  • Gonadotropin-Releasing Hormone / therapeutic use*
  • Gonadotropins / blood*
  • Hemochromatosis / blood
  • Hemochromatosis / complications
  • Hemochromatosis / drug therapy*
  • Humans
  • Hypogonadism / blood
  • Hypogonadism / drug therapy
  • Hypogonadism / etiology
  • Luteinizing Hormone / blood
  • Male
  • Middle Aged
  • Pituitary Gland / drug effects
  • Pituitary Gland / metabolism
  • Testosterone / blood*
  • Time Factors

Substances

  • Gonadotropins
  • Gonadotropin-Releasing Hormone
  • Testosterone
  • Luteinizing Hormone
  • Follicle Stimulating Hormone