Impaired negative selection of T cells in Hodgkin's disease antigen CD30-deficient mice

Cell. 1996 Feb 23;84(4):551-62. doi: 10.1016/s0092-8674(00)81031-4.

Abstract

CD30 is found on Reed-Sternberg cells of Hodgkin's disease and on a variety of non-Hodgkin's lymphoma cells and is up-regulated on cells after Epstein-Barr virus, human T cell leukemia virus, and HIV infections. We report here that the thymus in CD30-deficient mice contains elevated numbers of thymocytes. Activation-induced death of thymocytes after CD3 cross-linking is impaired both in vitro and in vivo. Breeding the CD30 mutation separately into alpha beta TCR-or gamma delta TCR-transgenic mice revealed a gross defect in negative but not positive selection. Thus, like TNF-receptors and Fas/Apo-1, the CD30 receptor is involved in cell death signaling. It is also an important coreceptor that participates in thymic deletion.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • B-Lymphocytes / cytology
  • B-Lymphocytes / immunology
  • Base Sequence
  • Cell Death / immunology
  • Cell Differentiation / genetics
  • Cell Differentiation / immunology
  • Cell Separation
  • Gene Deletion
  • Gene Expression / immunology
  • Hodgkin Disease / immunology
  • Ki-1 Antigen / genetics
  • Ki-1 Antigen / immunology*
  • Lymph Nodes / cytology
  • Male
  • Mice
  • Mice, Mutant Strains
  • Molecular Sequence Data
  • Receptors, Antigen, T-Cell, alpha-beta / genetics
  • Receptors, Antigen, T-Cell, alpha-beta / immunology
  • Receptors, Antigen, T-Cell, gamma-delta / genetics
  • Receptors, Antigen, T-Cell, gamma-delta / immunology
  • Signal Transduction / immunology
  • Superantigens / immunology
  • T-Lymphocytes / cytology
  • T-Lymphocytes / immunology*
  • T-Lymphocytes / ultrastructure
  • Thymus Gland / cytology
  • Thymus Gland / pathology

Substances

  • Ki-1 Antigen
  • Receptors, Antigen, T-Cell, alpha-beta
  • Receptors, Antigen, T-Cell, gamma-delta
  • Superantigens