Transcriptional map of the Treacher Collins candidate gene region

Genome Res. 1996 Jan;6(1):26-34. doi: 10.1101/gr.6.1.26.

Abstract

Treacher Collins syndrome (TCOF1) is a dominant disorder of craniofacial development that has been linked previosuly to a region of chromosome 5q31.3-32. Identification of recombination events in affected individuals has reduced the candidate gene region to a 0.5-Mb area between the loci RPS14 (proximal) and ANX6 [distal]. A transcriptional map of this candidate gene region, generated by analysis of exon amplification clones, has identified the genomic location of four genes, heparan sulfate-N-sulfotransferase-N-deacetylase, glutathione peroxidase, as well as two novel, previously uncharacterized genes. Each of these genes, based on their location, must be considered candidates for TCOF1 locus.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amidohydrolases / genetics
  • Amino Acid Sequence
  • Base Sequence
  • Chromosome Mapping*
  • DNA
  • Exons
  • Humans
  • Mandibulofacial Dysostosis / genetics*
  • Molecular Sequence Data
  • RNA, Messenger
  • Sulfotransferases / genetics
  • Transcription, Genetic

Substances

  • RNA, Messenger
  • DNA
  • Sulfotransferases
  • heparitin sulfotransferase
  • Amidohydrolases