Cryoglobulinemia in transfusion-dependent thalassemia major

Clin Exp Rheumatol. 1995 Nov-Dec:13 Suppl 13:S149-51.

Abstract

Objective: The aim of this study was to determine the frequency of cryoglobulinemia and associated symptoms in transfusion-dependent thalassemia patients at high risk for HCV infection.

Methods: A controlled epidemiological study was used to evaluate the prevalence of clinical, biochemical and immunological abnormalities in a group of 264 HCV-positive and 106 HCV-negative transfusion-dependent thalassemia patients. Haematologic and hepatic function tests were performed according to standard methods. HCV-RNA was detected by PCR analysis.

Results: The significant presence of cryoglobulinemia and associated symptoms (purpura, vasculitis, arthritis, asthenia, proteinuria), serum autoantibodies (SMA, anti-GOR, ANA, LKM), low complement and rheumatoid factor were found in HCV-positive compared with HCV-negative patients.

Conclusions: This study demonstrates the role of HCV in inducing cryoglobulinemia and immunological disorders in transfusion-dependent thalassemia patients. HCV infection and associated immune abnormalities are a new clinical aspect of, and deserve particular attention due to their high frequency in, transfusion-dependent thalassemia patients.

MeSH terms

  • Adolescent
  • Biomarkers
  • Child
  • Child, Preschool
  • Cryoglobulinemia / epidemiology
  • Cryoglobulinemia / etiology*
  • Hepatitis C / epidemiology
  • Hepatitis C / etiology*
  • Humans
  • Infant
  • Male
  • Prevalence
  • Risk Factors
  • Transfusion Reaction*
  • beta-Thalassemia / complications*
  • beta-Thalassemia / physiopathology
  • beta-Thalassemia / therapy

Substances

  • Biomarkers