This article, together with literatures, discusses one case of arrhythmia right ventricular dysplasia (ARVD) we treated. This disease should be taken into account in some arrhythmias from right ventricle, especially refractory arrhythmias in youths. Some non-invasive techniques such as echocardiography, cardial single photon emission computed tomography (SPECT), and magnetic resonance imaging (MRI) play more and more important role in the diagnosis of ARVD. These techniques can provide specific data for the early diagnosis.