Mitochondrial damage: an important feature in a number of inborn errors of metabolism?

J Inherit Metab Dis. 1996;19(2):140-2. doi: 10.1007/BF01799414.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antimetabolites / pharmacology
  • Buthionine Sulfoximine
  • Electron Transport Complex IV / metabolism
  • Glutathione / metabolism
  • Metabolism, Inborn Errors / metabolism*
  • Metabolism, Inborn Errors / pathology
  • Methionine Sulfoximine / analogs & derivatives
  • Methionine Sulfoximine / pharmacology
  • Mitochondria / drug effects
  • Mitochondria / metabolism*
  • Rats
  • Rats, Sprague-Dawley

Substances

  • Antimetabolites
  • Methionine Sulfoximine
  • Buthionine Sulfoximine
  • Electron Transport Complex IV
  • Glutathione