Alpha 2,3-specific desialylation of human red cells: effect on the autoantigens of the Pr, Sa and Sia-l1, -b1, -lb1 series

Vox Sang. 1998;74(2):109-12.

Abstract

Background and objectives: Pr1,2,3, PrM, Sa and Sia-l1, -b1, -lb1 are sialic acid (NeuNAc)-dependent antigens recognized by human cold agglutinins. Pr and Sa antigens are the O-glycans of glycophorins containing alpha 2,3NeuNAc (to galactose) and/or alpha 2,6NeuNAc (to galactosamine). The antigens of the Sia-l1, -b1, -lb1 complex are gangliosides that may carry alpha 2,3NeuNAc (to galactose) and/or alpha 2,8NeuNAc (to NeuNAc). We studied the NeuNAc groups involved in the antigens.

Materials and methods: From 74 sera with cold agglutinins against NeuNAc-dependent antigens, anti-T-free preparations were made and tested against human red cells, treated with an alpha 2,3-specific recombinant sialidase.

Results: Most (51/62) Pr antigens use alpha 2,3NeuNAc, some (8/62) use alpha 2,6NeuNAc and a few (3/62) use both sialyl groups as immunodominant components on glycophorins. The immunodominant component of Sa and Sia-l1, -b1, -lb1 determinants was alpha 2,3NeuNAc in all cases.

Conclusion: The red cell target structures for cold agglutinins against NeuNAc-dependent antigens have been identified. We propose a Pr nomenclature to reflect this. The binding of anti-Pr to gangliosides may be the basis for anti-Pr-induced peripheral neuropathy.

MeSH terms

  • Autoantigens / drug effects
  • Blood Group Antigens / immunology*
  • Epitopes
  • Erythrocytes / immunology*
  • Gangliosides / immunology
  • Glycophorins / drug effects
  • Glycophorins / immunology
  • Humans
  • Immunodominant Epitopes / blood
  • Immunodominant Epitopes / drug effects
  • N-Acetylneuraminic Acid / immunology
  • Neuraminidase / pharmacology
  • Sialic Acids / blood*
  • Sialic Acids / immunology
  • Sialoglycoproteins / blood
  • Sialoglycoproteins / immunology

Substances

  • Autoantigens
  • Blood Group Antigens
  • Epitopes
  • Gangliosides
  • Glycophorins
  • Immunodominant Epitopes
  • Sialic Acids
  • Sialoglycoproteins
  • Neuraminidase
  • N-Acetylneuraminic Acid