Fragile X premutation screening in women with premature ovarian failure

Hum Reprod. 1998 May;13(5):1184-7. doi: 10.1093/humrep/13.5.1184.

Abstract

We have screened 132 women with premature ovarian failure for fragile X (FRAXA) premutations. Three out of 23 (13%) pedigrees with the familial premature ovarian failure and 3/106 (3%) of women with the sporadic form of premature ovarian failure have FRAXA premutations compared with an expected prevalence of 1:590 (P=0.02). The mechanism of the association between FRAXA premutations and premature ovarian failure is unknown but as a genetic marker, FRAXA screening will be particularly valuable in predicting premature ovarian failure in some pedigrees and in the identification of families at risk of transmitting fragile X syndrome.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Female
  • Fragile X Mental Retardation Protein
  • Fragile X Syndrome / complications*
  • Fragile X Syndrome / diagnosis
  • Fragile X Syndrome / genetics*
  • Genetic Markers
  • Genetic Testing
  • Humans
  • Male
  • Minisatellite Repeats
  • Mutation*
  • Nerve Tissue Proteins / genetics
  • Ovary / pathology
  • Pedigree
  • Primary Ovarian Insufficiency / etiology*
  • Primary Ovarian Insufficiency / genetics*
  • Primary Ovarian Insufficiency / pathology
  • RNA-Binding Proteins*
  • Trinucleotide Repeats
  • X Chromosome / genetics

Substances

  • FMR1 protein, human
  • Genetic Markers
  • Nerve Tissue Proteins
  • RNA-Binding Proteins
  • Fragile X Mental Retardation Protein