Gastrointestinal perforation early after peripheral blood stem cell transplantation for AL amyloidosis

Bone Marrow Transplant. 1998 Aug;22(3):293-5. doi: 10.1038/sj.bmt.1701330.

Abstract

The morbidity and mortality of AL amyloidosis is caused by the deposition of Ig light chains as amyloid protein in vital organs. With conventional therapy median survival of patients with AL amyloidosis is 10-14 months. With high-dose chemotherapy clinical remissions of organ-specific disease have been reported. Here, we present a patient with high-risk AL amyloidosis who was given high-dose therapy and a peripheral blood stem cell transplant. Four days later she died of gastrointestinal perforation due to amyloid infiltrations.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Amyloidosis / immunology
  • Amyloidosis / pathology
  • Amyloidosis / therapy*
  • Fatal Outcome
  • Female
  • Hematopoietic Stem Cell Transplantation / adverse effects*
  • Humans
  • Immunoglobulin lambda-Chains / metabolism
  • Intestinal Perforation / etiology*
  • Intestinal Perforation / immunology
  • Intestinal Perforation / pathology
  • Transplantation, Autologous

Substances

  • Immunoglobulin lambda-Chains