Xid-like immunodeficiency in mice with disruption of the p85alpha subunit of phosphoinositide 3-kinase

Science. 1999 Jan 15;283(5400):390-2. doi: 10.1126/science.283.5400.390.

Abstract

Mice with a targeted gene disruption of p85alpha, a regulatory subunit of phosphoinositide 3-kinase, had impaired B cell development at the pro-B cell stage, reduced numbers of mature B cells and peritoneal CD5+ Ly-1 B cells, reduced B cell proliferative responses, and no T cell-independent antibody production. These phenotypes are nearly identical to those of Btk-/- or xid (X-linked immunodeficiency) mice. These results provide evidence that p85alpha is functionally linked to the Btk pathway in antigen receptor-mediated signal transduction and is pivotal in B cell development and functions.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Agammaglobulinaemia Tyrosine Kinase
  • Animals
  • Antibody Formation
  • Antigens, Ly / analysis
  • Antigens, T-Independent / immunology
  • B-Lymphocyte Subsets / cytology
  • B-Lymphocyte Subsets / immunology
  • B-Lymphocytes / cytology
  • B-Lymphocytes / immunology*
  • Bone Marrow / immunology
  • CD5 Antigens / analysis
  • Cell Survival
  • Gene Targeting
  • Genetic Linkage
  • Immunologic Deficiency Syndromes / enzymology*
  • Immunologic Deficiency Syndromes / genetics
  • Immunologic Deficiency Syndromes / immunology
  • Lymphocyte Count
  • Lymphoid Tissue / immunology
  • Mice
  • Mutation
  • Phenotype
  • Phosphatidylinositol 3-Kinases / genetics
  • Phosphatidylinositol 3-Kinases / metabolism*
  • Protein-Tyrosine Kinases / genetics
  • Protein-Tyrosine Kinases / metabolism
  • Signal Transduction
  • T-Lymphocytes / immunology
  • X Chromosome

Substances

  • Antigens, Ly
  • Antigens, T-Independent
  • CD5 Antigens
  • Phosphatidylinositol 3-Kinases
  • Protein-Tyrosine Kinases
  • Agammaglobulinaemia Tyrosine Kinase
  • Btk protein, mouse