Paulson HL - Search Results

1

Pathogenesis of SCA3 and implications for other polyglutamine diseases.

McLoughlin HS, Moore LR, Paulson HL. McLoughlin HS, et al. Among authors: paulson hl. Neurobiol Dis. 2020 Feb;134:104635. doi: 10.1016/j.nbd.2019.104635. Epub 2019 Oct 24. Neurobiol Dis. 2020. PMID: 31669734 Free PMC article. Review.

2

In vivo suppression of polyglutamine neurotoxicity by C-terminus of Hsp70-interacting protein (CHIP) supports an aggregation model of pathogenesis.

Williams AJ, Knutson TM, Colomer Gould VF, Paulson HL. Williams AJ, et al. Among authors: paulson hl. Neurobiol Dis. 2009 Mar;33(3):342-53. doi: 10.1016/j.nbd.2008.10.016. Epub 2008 Nov 8. Neurobiol Dis. 2009. PMID: 19084066 Free PMC article.

3

RNA-mediated neurodegeneration in repeat expansion disorders.

Todd PK, Paulson HL. Todd PK, et al. Among authors: paulson hl. Ann Neurol. 2010 Mar;67(3):291-300. doi: 10.1002/ana.21948. Ann Neurol. 2010. PMID: 20373340 Free PMC article. Review.

4

Activity and cellular functions of the deubiquitinating enzyme and polyglutamine disease protein ataxin-3 are regulated by ubiquitination at lysine 117.

Todi SV, Scaglione KM, Blount JR, Basrur V, Conlon KP, Pastore A, Elenitoba-Johnson K, Paulson HL. Todi SV, et al. Among authors: paulson hl. J Biol Chem. 2010 Dec 10;285(50):39303-13. doi: 10.1074/jbc.M110.181610. Epub 2010 Oct 13. J Biol Chem. 2010. PMID: 20943656 Free PMC article.

5

Machado-Joseph disease/spinocerebellar ataxia type 3.

Paulson H. Paulson H. Handb Clin Neurol. 2012;103:437-49. doi: 10.1016/B978-0-444-51892-7.00027-9. Handb Clin Neurol. 2012. PMID: 21827905 Free PMC article. Review.

6

Early changes in cerebellar physiology accompany motor dysfunction in the polyglutamine disease spinocerebellar ataxia type 3.

Shakkottai VG, do Carmo Costa M, Dell'Orco JM, Sankaranarayanan A, Wulff H, Paulson HL. Shakkottai VG, et al. Among authors: paulson hl. J Neurosci. 2011 Sep 7;31(36):13002-14. doi: 10.1523/JNEUROSCI.2789-11.2011. J Neurosci. 2011. PMID: 21900579 Free PMC article.

7

Toward understanding Machado-Joseph disease.

Costa Mdo C, Paulson HL. Costa Mdo C, et al. Among authors: paulson hl. Prog Neurobiol. 2012 May;97(2):239-57. doi: 10.1016/j.pneurobio.2011.11.006. Epub 2011 Nov 23. Prog Neurobiol. 2012. PMID: 22133674 Free PMC article. Review.

8

Toward RNAi therapy for the polyglutamine disease Machado-Joseph disease.

Costa Mdo C, Luna-Cancalon K, Fischer S, Ashraf NS, Ouyang M, Dharia RM, Martin-Fishman L, Yang Y, Shakkottai VG, Davidson BL, Rodríguez-Lebrón E, Paulson HL. Costa Mdo C, et al. Among authors: paulson hl. Mol Ther. 2013 Oct;21(10):1898-908. doi: 10.1038/mt.2013.144. Epub 2013 Jun 14. Mol Ther. 2013. PMID: 23765441 Free PMC article.

9

A knockin mouse model of spinocerebellar ataxia type 3 exhibits prominent aggregate pathology and aberrant splicing of the disease gene transcript.

Ramani B, Harris GM, Huang R, Seki T, Murphy GG, Costa Mdo C, Fischer S, Saunders TL, Xia G, McEachin RC, Paulson HL. Ramani B, et al. Among authors: paulson hl. Hum Mol Genet. 2015 Mar 1;24(5):1211-24. doi: 10.1093/hmg/ddu532. Epub 2014 Oct 15. Hum Mol Genet. 2015. PMID: 25320121 Free PMC article.

10

Differential recruitment of UBQLN2 to nuclear inclusions in the polyglutamine diseases HD and SCA3.

Zeng L, Wang B, Merillat SA, Minakawa EN, Perkins MD, Ramani B, Tallaksen-Greene SJ, Costa MDC, Albin RL, Paulson HL. Zeng L, et al. Among authors: paulson hl. Neurobiol Dis. 2015 Oct;82:281-288. doi: 10.1016/j.nbd.2015.06.017. Epub 2015 Jun 30. Neurobiol Dis. 2015. PMID: 26141599 Free PMC article.

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