Post transplant CD8+ gammadelta T-cell lymphoma associated with human herpes virus-6 infection

Leuk Lymphoma. 1999 Apr;33(3-4):377-84. doi: 10.3109/10428199909058439.

Abstract

Gammadelta T-cell lymphoma is a rare T-cell lymphoproliferative disorder that has been reported in both immunocompetent and immunocompromised persons. This report describes a forty eight year old patient who developed gammadelta T-cell lymphoma four years after undergoing living-related kidney transplantation. The lymphoma expressed CD2, CD3, CD7, CD8 and CD56, and the gammadelta T-cell receptor and did not express CD5, CD4 and the alphabeta T-cell receptor. In addition, HHV-6 was cultured from the patient's bone marrow, marking the first time that this virus has been associated with gammadelta T-cell lymphoma. Since all patients with gammadelta T-cell lymphoma described to date have responded poorly to standard combination chemotherapies, the patient was treated with the purine analogue 2-chlorodeoxyadenosine. While he responded transiently to treatment, long term remission was not achieved indicating that additional therapeutic approches still need to be developed, for the management of this disorder.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Antigens, CD / analysis*
  • Antigens, CD / genetics
  • Antineoplastic Agents / therapeutic use
  • Bone Marrow / immunology
  • Bone Marrow / pathology
  • Bone Marrow / virology
  • CD8 Antigens / analysis
  • CD8-Positive T-Lymphocytes / immunology*
  • Cladribine / therapeutic use
  • Glomerulonephritis, IGA / complications
  • Glomerulonephritis, IGA / surgery
  • Herpesviridae Infections / complications*
  • Herpesvirus 6, Human* / isolation & purification
  • Humans
  • Kidney Failure, Chronic / etiology
  • Kidney Failure, Chronic / surgery
  • Kidney Transplantation*
  • Lymphoma, T-Cell / drug therapy
  • Lymphoma, T-Cell / etiology
  • Lymphoma, T-Cell / immunology*
  • Lymphoma, T-Cell / pathology
  • Male
  • Middle Aged
  • Postoperative Complications
  • Receptors, Antigen, T-Cell, gamma-delta / biosynthesis*
  • Receptors, Antigen, T-Cell, gamma-delta / genetics

Substances

  • Antigens, CD
  • Antineoplastic Agents
  • CD8 Antigens
  • Receptors, Antigen, T-Cell, gamma-delta
  • Cladribine