Allelic exclusion of the T cell receptor beta locus requires the SH2 domain-containing leukocyte protein (SLP)-76 adaptor protein

J Exp Med. 1999 Oct 18;190(8):1093-102. doi: 10.1084/jem.190.8.1093.

Abstract

Signaling via the pre-T cell receptor (TCR) is required for the proliferative expansion and maturation of CD4(-)CD8(-) double-negative (DN) thymocytes into CD4(+)CD8(+) double-positive (DP) cells and for TCR-beta allelic exclusion. The adaptor protein SH2 domain-containing leukocyte protein (SLP)-76 has been shown to play a crucial role in thymic development, because thymocytes of SLP-76(-/-) mice are arrested at the CD25(+)CD44(-) DN stage. Here we show that SLP-76(-/-) DN thymocytes express the pre-TCR on their surfaces and that introduction of a TCR-alpha/beta transgene into the SLP-76(-/-) background fails to cause expansion of DN thymocytes or developmental progression to the DP stage. Moreover, analysis of TCR-beta rearrangement in SLP-76(-/-) TCR-transgenic mice or in single CD25(+)CD44(-) DN cells from SLP-76(-/-) mice indicates an essential role of SLP-76 in TCR-beta allelic exclusion.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adaptor Proteins, Signal Transducing
  • Alleles
  • Animals
  • Antigens, CD / genetics
  • Antigens, CD / immunology
  • Cell Line
  • Flow Cytometry
  • Gene Expression Regulation
  • Gene Rearrangement
  • Mice
  • Mice, Transgenic
  • Phosphoproteins / immunology*
  • Receptors, Antigen, T-Cell, alpha-beta / genetics*
  • Receptors, Antigen, T-Cell, alpha-beta / immunology
  • Signal Transduction / immunology
  • src Homology Domains / immunology*

Substances

  • Adaptor Proteins, Signal Transducing
  • Antigens, CD
  • Phosphoproteins
  • Receptors, Antigen, T-Cell, alpha-beta
  • SLP-76 signal Transducing adaptor proteins