Hepatosplenic B-cell lymphoma associated with hemophagocytic syndrome: a case report

J Korean Med Sci. 1999 Dec;14(6):671-4. doi: 10.3346/jkms.1999.14.6.671.

Abstract

While T-cell non-Hodgkin's lymphoma (NHL) associated with hemophagocytic syndrome (HPS) has been frequently observed, B-cell NHL associated with HPS has been rarely reported. We report a case of hepatosplenic B-cell lymphoma associated with HPS in a 41-year-old woman who presented with fever of unknown origin. An abdominal CT scan revealed splenomegaly with focal splenic infarction. Splenectomy and a liver wedge biopsy showed sinusoidal-pattern infiltration of medium to large tumor cells with positive reaction to a B-lymphocyte marker. Findings on bone marrow examination showed proliferation of histiocytes with avid hemophagocytosis.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Antigens, CD / analysis
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Biomarkers, Tumor / analysis
  • Bone Marrow Cells / pathology
  • Female
  • Histiocytosis, Non-Langerhans-Cell / complications*
  • Histiocytosis, Non-Langerhans-Cell / pathology
  • Humans
  • Liver Neoplasms / complications*
  • Liver Neoplasms / diagnostic imaging
  • Liver Neoplasms / pathology
  • Lymphoma, B-Cell / complications*
  • Lymphoma, B-Cell / diagnostic imaging
  • Lymphoma, B-Cell / pathology
  • Splenic Neoplasms / complications*
  • Splenic Neoplasms / diagnostic imaging
  • Splenic Neoplasms / pathology
  • Splenomegaly / diagnostic imaging
  • Tomography, X-Ray Computed

Substances

  • Antigens, CD
  • Biomarkers, Tumor