gamma-catenin is regulated by the APC tumor suppressor and its oncogenic activity is distinct from that of beta-catenin

Genes Dev. 2000 Jun 1;14(11):1319-31.

Abstract

beta-Catenin and gamma-catenin (plakoglobin), vertebrate homologs of Drosophila armadillo, function in cell adhesion and the Wnt signaling pathway. In colon and other cancers, mutations in the APC tumor suppressor protein or beta-catenin's amino terminus stabilize beta-catenin, enhancing its ability to activate transcription of Tcf/Lef target genes. Though beta- and gamma-catenin have analogous structures and functions and like binding to APC, evidence that gamma-catenin has an important role in cancer has been lacking. We report here that APC regulates both beta- and gamma-catenin and gamma-catenin functions as an oncogene. In contrast to beta-catenin, for which only amino-terminal mutated forms transform RK3E epithelial cells, wild-type and several amino-terminal mutated forms of gamma-catenin had similar transforming activity. gamma-Catenin's transforming activity, like beta-catenin's, was dependent on Tcf/Lef function. However, in contrast to beta-catenin, gamma-catenin strongly activated c-Myc expression and c-Myc function was crucial for gamma-catenin transformation. Our findings suggest APC mutations alter regulation of both beta- and gamma-catenin, perhaps explaining why the frequency of APC mutations in colon cancer far exceeds that of beta-catenin mutations. Elevated c-Myc expression in cancers with APC defects may be due to altered regulation of both beta- and gamma-catenin. Furthermore, the data imply beta- and gamma-catenin may have distinct roles in Wnt signaling and cancer via differential effects on downstream target genes.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adenomatous Polyposis Coli Protein
  • Alleles
  • Animals
  • Cell Adhesion
  • Cell Division
  • Cell Line
  • Cell Line, Transformed
  • Colonic Neoplasms / metabolism
  • Cytoskeletal Proteins / genetics
  • Cytoskeletal Proteins / metabolism*
  • Cytoskeletal Proteins / physiology
  • DNA-Binding Proteins / metabolism
  • Desmoplakins
  • Fluorescent Antibody Technique
  • Gene Expression Regulation
  • Humans
  • Lymphoid Enhancer-Binding Factor 1
  • Mice
  • Mice, Nude
  • Mutation
  • Neoplasm Transplantation
  • Neoplasms / metabolism*
  • Proto-Oncogene Proteins / metabolism
  • Proto-Oncogene Proteins c-myc / biosynthesis
  • Signal Transduction
  • Time Factors
  • Trans-Activators*
  • Transcription Factors / metabolism
  • Transcription, Genetic
  • Tumor Cells, Cultured
  • Wnt Proteins
  • Zebrafish Proteins*
  • beta Catenin
  • gamma Catenin

Substances

  • Adenomatous Polyposis Coli Protein
  • CTNNB1 protein, human
  • CTNNB1 protein, mouse
  • Cytoskeletal Proteins
  • DNA-Binding Proteins
  • Desmoplakins
  • JUP protein, human
  • Jup protein, mouse
  • Lymphoid Enhancer-Binding Factor 1
  • Proto-Oncogene Proteins
  • Proto-Oncogene Proteins c-myc
  • Trans-Activators
  • Transcription Factors
  • Wnt Proteins
  • Zebrafish Proteins
  • beta Catenin
  • gamma Catenin