The role of suppressor cells in the pathogenesis of common variable hypogammaglobulinemia and the immunodeficiency associated with myeloma

Fed Proc. 1976 Jul;35(9):2067-72.

Abstract

The role of suppressor cells in the pathogenesis of immunodeficiency was analyzed using a technique that permits study of the differentiation of B lymphocytes into immunoglobulin-synthesizing plasma cells. Lymphocytes from normals synthesized 4,910 ng of IgM, 1,270 ng of IgA, and 1,625 ng of IgG per 2 X 10(6) cells when cultured for 7 days in the presence of pokeweed mitogen. In contrast the lymphocytes from patients with common variable hypogammaglobulinemia did not synthesize significant quantities of immunoglobulin. When lymphocytes from 9 of 13 patients with common variable hypogammaglobulinemia studied were cocultured with normal lymphocytes, the synthesis of immunoglobulin by the normal lymphocytes was depressed by 75-100%. A comparable suppression of immunoglobulin synthesis by normal lymphocytes was observed when they were cocultured with T cells from hypogammaglobulinemic patients. These studies suggest that in some patients the disease common variable hypogammaglobulinemia may not be due to an intrinsic defect of B cells alone but may be cuased or perpetuated by an abnormality of regulatory T cells that act to suppress B-cell maturation and antibody production. Peripheral blood lymphocytes from myeloma patients also had a drastically reduced capacity to produce polyclonal immunoglobulins. Three of 6 myeloma patients tested had circulating mononuclear cells that suppressed immunoglobulin production by cocultured normal lymphocytes. Purified T cells from myeloma patients did not mediate this suppressor effect. These observations suggest that one mechanism for the humoral immune deficiency observed in myeloma patients is a block of polyclonal B-cell maturation by suppressor cells.

MeSH terms

  • Agammaglobulinemia / drug therapy
  • Agammaglobulinemia / genetics
  • Agammaglobulinemia / immunology*
  • Antibody Formation*
  • Antibody-Producing Cells / immunology
  • B-Lymphocytes / immunology*
  • Cell Differentiation
  • Genetic Linkage
  • Humans
  • Immunoglobulin A / biosynthesis
  • Immunoglobulin G / biosynthesis
  • Immunoglobulin M / biosynthesis
  • Immunosuppression Therapy*
  • Mitogens
  • Models, Biological
  • Multiple Myeloma / immunology*
  • Prednisone / therapeutic use
  • Sex Chromosomes
  • T-Lymphocytes / immunology*
  • Thymoma / complications
  • Thymoma / immunology

Substances

  • Immunoglobulin A
  • Immunoglobulin G
  • Immunoglobulin M
  • Mitogens
  • Prednisone