Steroid-sensitive nephrotic syndrome associated with Kimura disease

C Nakahara; T Wada; J Kusakari; K Kanemoto; H Kinugasa; M Sibasaki; M Nagata; A Matsui

doi:10.1007/s004670050798

Steroid-sensitive nephrotic syndrome associated with Kimura disease

Pediatr Nephrol. 2000 Jun;14(6):482-5. doi: 10.1007/s004670050798.

Authors

C Nakahara¹, T Wada, J Kusakari, K Kanemoto, H Kinugasa, M Sibasaki, M Nagata, A Matsui

Affiliation

¹ Department of Pediatrics, Tsukuba University Hospital, University of Tsukuba, Ibaraki, Japan. [email protected]

PMID: 10872189
DOI: 10.1007/s004670050798

Abstract

We report an 11-year-old Japanese boy with Kimura disease and associated nephrotic syndrome. Before the diagnosis of Kimura disease was established, the patient had three episodes of swelling on the left cheek with subsequent nephrotic syndrome. Steroids were effective for both conditions. However, both conditions recurred within months of discontinuation of steroids. For the fourth episode of swelling on the left cheek, cyclosporine (CsA) was used. The subcutaneous tumor responded to CsA and disappeared within a few days. There has been no subsequent relapse of the nephrotic syndrome to date.

Publication types

Case Reports

MeSH terms

Angiolymphoid Hyperplasia with Eosinophilia / complications*
Angiolymphoid Hyperplasia with Eosinophilia / drug therapy
Angiolymphoid Hyperplasia with Eosinophilia / pathology
Anti-Inflammatory Agents / therapeutic use
Child
Cyclosporine / therapeutic use
Humans
Immunosuppressive Agents / therapeutic use
Magnetic Resonance Imaging
Male
Nephrotic Syndrome / complications*
Nephrotic Syndrome / drug therapy*
Nephrotic Syndrome / pathology
Prednisolone / therapeutic use
Recurrence
Steroids / therapeutic use*

Substances

Anti-Inflammatory Agents
Immunosuppressive Agents
Steroids
Cyclosporine
Prednisolone