CD8(+) T cell-mediated skin disease in mice lacking IRF-2, the transcriptional attenuator of interferon-alpha/beta signaling

Immunity. 2000 Nov;13(5):643-55. doi: 10.1016/s1074-7613(00)00064-9.

Abstract

The balanced action of cytokines is known to be critical for the maintenance of homeostatic immune responses. Here, we report the development of an inflammatory skin disease involving CD8(+) T cells, in mice lacking the transcription factor, interferon regulatory factor-2 (IRF-2). CD8(+) T cells exhibit in vitro hyper-responsiveness to antigen stimulation, accompanied with a notable upregulation of the expression of genes induced by interferon-alpha/beta (IFN-alpha/beta). Furthermore, both disease development and CD8(+) T cell abnormality are suppressed by the introduction of nullizygosity to the genes that positively regulate the IFN-alpha/beta signaling pathway. IRF-2 may represent a unique negative regulator, attenuating IFN-alpha/beta-induced gene transcription, which is necessary for balancing the beneficial and harmful effects of IFN-alpha/beta signaling in the immune system.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • CD8-Positive T-Lymphocytes / immunology*
  • Cytotoxicity, Immunologic
  • DNA-Binding Proteins / genetics*
  • DNA-Binding Proteins / immunology*
  • Gene Expression Regulation / immunology
  • Interferon Regulatory Factor-2
  • Interferons / genetics
  • Interferons / immunology*
  • Mice
  • Mice, Knockout
  • Repressor Proteins*
  • Signal Transduction / genetics
  • Signal Transduction / immunology*
  • Skin Diseases / etiology
  • Skin Diseases / genetics
  • Skin Diseases / immunology*
  • Transcription Factors / genetics
  • Transcription Factors / immunology

Substances

  • DNA-Binding Proteins
  • Interferon Regulatory Factor-2
  • Irf2 protein, mouse
  • Repressor Proteins
  • Transcription Factors
  • Interferons