LIS1 regulates CNS lamination by interacting with mNudE, a central component of the centrosome

Neuron. 2000 Dec;28(3):665-79. doi: 10.1016/s0896-6273(00)00145-8.

Abstract

LIS1, a microtubule-associated protein, is required for neuronal migration, but the precise mechanism of LIS1 function is unknown. We identified a LIS1 interacting protein encoded by a mouse homolog of NUDE, a nuclear distribution gene in A. nidulans and a multicopy suppressor of the LIS1 homolog, NUDF. mNudE is located in the centrosome or microtubule organizing center (MTOC), and interacts with six different centrosomal proteins. Overexpression of mNudE dissociates gamma-tubulin from the centrosome and disrupts microtubule organization. Missense mutations that disrupt LIS1 function block LIS1-mNudE binding. Moreover, misexpression of the LIS1 binding domain of mNudE in Xenopus embryos disrupts the architecture and lamination of the CNS. Thus, LIS1-mNudE interactions may regulate neuronal migration through dynamic reorganization of the MTOC.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • 1-Alkyl-2-acetylglycerophosphocholine Esterase
  • Animals
  • COS Cells
  • Central Nervous System / embryology*
  • Central Nervous System / metabolism*
  • Centrosome / metabolism*
  • Embryo, Nonmammalian / abnormalities
  • Embryo, Nonmammalian / pathology
  • Fungal Proteins / genetics
  • Fungal Proteins / metabolism*
  • Gene Expression Regulation, Developmental
  • Mice
  • Microtubule-Associated Proteins / genetics
  • Microtubule-Associated Proteins / metabolism*
  • Molecular Sequence Data
  • Mutagenesis, Site-Directed
  • Protein Binding / genetics
  • Protein Structure, Tertiary / genetics
  • RNA, Messenger / biosynthesis
  • Sequence Homology, Amino Acid
  • Substrate Specificity / physiology
  • Tubulin / metabolism
  • Two-Hybrid System Techniques
  • Xenopus

Substances

  • Fungal Proteins
  • Microtubule-Associated Proteins
  • RNA, Messenger
  • RO-11 protein, Neurospora crassa
  • Tubulin
  • 1-Alkyl-2-acetylglycerophosphocholine Esterase
  • Pafah1b1 protein, mouse

Associated data

  • GENBANK/AF322073