Primary Sjögren's syndrome--treatment of fetal incomplete atrioventricular block with dexamethasone

J Rheumatol. 2001 Feb;28(2):373-6.

Abstract

Pregnancies in women with autoantibodies against Ro/SSA and/or La/SSB may be associated with permanent and treatment resistant fetal atrioventricular (AV) block. We describe a patient with primary S ogren's syndrome and anti-Ro (60 kDa and 52 kDa) and anti-La autoantibodies, in whom fetal bradycardia with second-degree AV block was detected at 19 + 0 weeks of gestation. Maternal treatment with dexamethasone (4 mg/day po) was started 2 days later. The baby's heart rate improved gradually, returning to normal after about 6 weeks of treatment. Our case illustrates the importance of close monitoring of the fetal heart rate in risk-pregnancies from about week 16 of gestation and initiation of dexamethasone treatment without delay when a block is detected.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Anti-Inflammatory Agents / administration & dosage*
  • Anti-Inflammatory Agents / adverse effects
  • Antibodies, Antinuclear / adverse effects
  • Antibodies, Antinuclear / blood
  • Antibodies, Antinuclear / immunology
  • Dexamethasone / administration & dosage*
  • Dexamethasone / adverse effects
  • Female
  • Fetal Diseases / diagnosis
  • Fetal Diseases / drug therapy
  • Fetal Diseases / immunology*
  • Heart Block / congenital*
  • Heart Block / drug therapy
  • Heart Block / immunology*
  • Humans
  • Pregnancy
  • Pregnancy Complications / diagnosis
  • Pregnancy Complications / drug therapy
  • Pregnancy Complications / immunology*
  • Sjogren's Syndrome / complications*
  • Sjogren's Syndrome / immunology
  • Sjogren's Syndrome / physiopathology
  • Treatment Outcome

Substances

  • Anti-Inflammatory Agents
  • Antibodies, Antinuclear
  • SS-A antibodies
  • Dexamethasone