Hypocomplementemic urticarial vasculitis and lower cranial nerve palsies

J Assoc Physicians India. 2000 May;48(5):536-7.

Abstract

A 55 years post menopausal lady presented with puffiness of face, and a pruritic urticarial rash over face and upper trunk of one week duration with accompanying dysphagia. Clinical examination revealed an urticarial rash over face and upper trunk, two small ulcers over floor of mouth and evidence of bilateral VIII, IX and Xth cranial nerve palsies. Hypocomplementemia, negative immune profile and evidence of vasculitis on skin biopsy suggested a diagnosis of hypocomplementemic urticarial vasculitis. The patient responded to a course of steroids.

Publication types

  • Case Reports

MeSH terms

  • Complement C3 / deficiency*
  • Complement C4 / deficiency*
  • Cranial Nerve Diseases / diagnosis*
  • Cranial Nerve Diseases / immunology
  • Diagnosis, Differential
  • Female
  • Humans
  • Middle Aged
  • Urticaria / diagnosis*
  • Urticaria / immunology
  • Vasculitis, Leukocytoclastic, Cutaneous / diagnosis*
  • Vasculitis, Leukocytoclastic, Cutaneous / immunology

Substances

  • Complement C3
  • Complement C4