The TEL-Jak2 oncoprotein induces Socs1 expression and altered cytokine response in Ba/F3 cells

Oncogene. 2001 Feb 15;20(7):849-58. doi: 10.1038/sj.onc.1204201.

Abstract

The leukemia-associated TEL-Jak2 fusion protein possesses a constitutive tyrosine kinase activity and transforming properties in hematopoietic cell lines and animal models. In the murine pro-B Ba/F3 cell line, this fusion constitutively activates the Signal Transducer and Activator of Transcription 5 (Stat5) factors and, as a consequence, induces the sustained expression of various Stat5-target genes including the Cytokine Inducible SH2-containing protein (Cis) gene, which codes for a member of the Suppressor of Cytokine Signaling (Socs) protein family. In TEL-Jak2-transformed Ba/F3 cells, we also observed the upregulation of the Socs1 gene, whose product has been reported to negatively regulate the Jak kinase activity. In transient transfection experiments, Socs1 physically interacts with TEL-Jak2 and interferes with the TEL-Jak2-induced phosphorylation and activation of Stat5 factors, probably through the Socs1-induced proteasome-mediated degradation of the fusion protein. Interestingly, TEL-Jak2-expressing Ba/F3 cells were found to be resistant to the anti-proliferative activities of gamma interferon (IFN-gamma) seemingly as a consequence of Socs1 constitutive expression. These results indicate that the Socs1-dependent cytokine feedback loop, although active, is bypassed by the TEL-Jak2 fusion, but may play a role in the leukemogenic process by altering the cytokine responses of the leukemic cells. Our results also suggest that Socs1 plays a role in shutting down the signaling from the normally activated Jak2 kinase by inducing its proteasome-dependent degradation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • B-Lymphocytes / metabolism
  • Carrier Proteins / biosynthesis*
  • Cell Line, Transformed
  • Cells, Cultured
  • Cysteine Endopeptidases / metabolism
  • Cytokines / biosynthesis*
  • Gene Expression Regulation, Leukemic
  • Hematopoietic Stem Cells / metabolism
  • Interferon gamma Receptor
  • Janus Kinase 2
  • Mice
  • Multienzyme Complexes / metabolism
  • Oncogene Proteins, Fusion / metabolism*
  • Proteasome Endopeptidase Complex
  • Protein Binding
  • Protein-Tyrosine Kinases / metabolism*
  • Proto-Oncogene Proteins*
  • Receptors, Interferon / metabolism
  • Repressor Proteins / biosynthesis*
  • Signal Transduction
  • Suppressor of Cytokine Signaling 1 Protein
  • Suppressor of Cytokine Signaling Proteins
  • Ubiquitins / metabolism

Substances

  • Carrier Proteins
  • Cytokines
  • Multienzyme Complexes
  • Oncogene Proteins, Fusion
  • Proto-Oncogene Proteins
  • Receptors, Interferon
  • Repressor Proteins
  • Socs1 protein, mouse
  • Suppressor of Cytokine Signaling 1 Protein
  • Suppressor of Cytokine Signaling Proteins
  • TEL-JAK2 fusion protein, human
  • TEL-JAK2 fusion protein, mouse
  • Ubiquitins
  • Protein-Tyrosine Kinases
  • JAK2 protein, human
  • Jak2 protein, mouse
  • Janus Kinase 2
  • Cysteine Endopeptidases
  • Proteasome Endopeptidase Complex