A genetically tractable model of human glioma formation

Cancer Res. 2001 May 1;61(9):3556-60.

Abstract

Gliomas remain one of the deadliest forms of cancer. Improved therapeutics will require a better understanding of the molecular nature of these tumors. We, therefore, mimicked the most common genetic changes found in grade III-IV gliomas, disruption of the p53 and RB pathways and activation of telomere maintenance and independence from growth factors, through the ectopic expression of the SV40 T/t-Ag oncogene, an oncogenic form of H-ras (H-ras(V12G)), and the human telomerase catalytic subunit hTERT in normal human astrocytes. The resulting cells displayed many of the hallmarks of grade III-IV gliomas, including greatly expanded life span and growth in soft agar and, most importantly, were tumorigenic with pathology consistent with grade III-IV neuroectodermal tumors in mice. This model system will, for the first time, allow the biological significance of selected genetic alterations to be studied in human gliomas.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Antigens, Polyomavirus Transforming / biosynthesis
  • Antigens, Polyomavirus Transforming / genetics
  • Astrocytes / metabolism
  • Astrocytes / pathology
  • Astrocytes / physiology
  • Catalytic Domain
  • Cell Transformation, Viral / genetics*
  • DNA-Binding Proteins
  • Genes, ras
  • Glioma / genetics*
  • Glioma / pathology
  • Humans
  • Mice
  • Mice, Inbred BALB C
  • Mice, Nude
  • Mice, SCID
  • RNA*
  • Retroviridae / genetics
  • Telomerase / biosynthesis
  • Telomerase / genetics
  • Tumor Cells, Cultured

Substances

  • Antigens, Polyomavirus Transforming
  • DNA-Binding Proteins
  • telomerase RNA
  • RNA
  • Telomerase