Budd-Chiari syndrome secondary to intracardiac extension of hepatocellular carcinoma. Two cases treated by radical resection

J Saïsse; J Hardwigsen; P Castellani; T Caus; Y P Le Treut

Budd-Chiari syndrome secondary to intracardiac extension of hepatocellular carcinoma. Two cases treated by radical resection

Hepatogastroenterology. 2001 May-Jun;48(39):836-9.

Authors

J Saïsse¹, J Hardwigsen, P Castellani, T Caus, Y P Le Treut

Affiliation

¹ Department of Surgery and Liver Transplantation, Hôpital de La Conception, 147 Boulevard Baille, 13385 Marseille, France.

PMID: 11462935

Abstract

Two young women presenting Budd-Chiari syndrome as the primary manifestation of hepatocellular carcinoma with intracardiac extension were treated by debulking of the atrium and inferior vena cava under extracorporeal circulation and major hepatectomy. The first patient who was treated in a single procedure died during the immediate postoperative period. The second patient who was treated in two steps died of meningeal and pulmonary metastases 12 months later. Clinical findings and surgical strategy for this rare condition are discussed in the light of 6 previously reported surgical cases.

Publication types

Case Reports
Review

MeSH terms

Adult
Budd-Chiari Syndrome / diagnosis
Budd-Chiari Syndrome / etiology*
Budd-Chiari Syndrome / mortality
Budd-Chiari Syndrome / surgery
Carcinoma, Hepatocellular / diagnosis
Carcinoma, Hepatocellular / mortality
Carcinoma, Hepatocellular / secondary*
Carcinoma, Hepatocellular / surgery
Diagnostic Imaging
Fatal Outcome
Female
Heart Atria / pathology
Heart Atria / surgery
Heart Neoplasms / diagnosis
Heart Neoplasms / mortality
Heart Neoplasms / secondary*
Heart Neoplasms / surgery
Humans
Liver Neoplasms / diagnosis*
Liver Neoplasms / mortality
Liver Neoplasms / surgery
Middle Aged
Neoplastic Cells, Circulating
Survival Rate
Vena Cava, Inferior / pathology
Vena Cava, Inferior / surgery