Statistical mechanics of prion diseases

Phys Rev Lett. 2001 Jul 30;87(5):058101. doi: 10.1103/PhysRevLett.87.058101. Epub 2001 Jul 12.

Abstract

We present a two-dimensional, lattice based, protein-level statistical mechanical model for prion diseases (e.g., mad cow disease) with concomitant prion protein misfolding and aggregation. Our studies lead us to the hypothesis that the observed broad incubation time distribution in epidemiological data reflect fluctuation dominated growth seeded by a few nanometer scale aggregates, while much narrower incubation time distributions for innoculated lab animals arise from statistical self-averaging. We model "species barriers" to prion infection and assess a related treatment protocol.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Animals
  • Computer Simulation
  • Cricetinae
  • Humans
  • Mice
  • Models, Biological*
  • Models, Statistical*
  • Prion Diseases* / epidemiology
  • Prion Diseases* / metabolism
  • Prion Diseases* / transmission
  • Prions / chemistry
  • Prions / metabolism
  • Protein Folding

Substances

  • Prions